The rice ufra disease, caused by Ditylenchus angustus, is one of the important rice diseases that can cause severe yield loss. D. angustus is the quarantined pest in China. Ufra disease has seriously damaged rice production in countries such as Bangladesh, India and Myanmar. Here, we summarized the research progress of rice ufra disease in terms of its biology, morphology, distribution of D. angustus, as well as symptoms on rice in the field. This information is of significance for carrying out plant quarantine and management in China.